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What is Anotia?

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  • Written By: Mary McMahon
  • Edited By: O. Wallace
  • Last Modified Date: 13 September 2016
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Anotia is a very rare congenital anomaly in which the external part of the ear is entirely absent. It is difficult to determine the incidence of anotia, because this birth defect is often bundled in with microtia, in which part of the ear is missing, for the purpose of keeping statistics. There are no obvious risk factors for anotia, and sometimes it may occur as part of a congenital condition or syndrome, in which a variety of other anomalies may present themselves as well.

In true anotia, where the auricle of the ear is missing, the patient is usually diagnosed very soon after birth. A doctor may recommend follow up exams to check the baby's hearing, because anotia is sometimes associated with hearing damage. Surgery to reconstruct the ear is recommended between the ages of five and seven, after the child has had a chance to mature slightly, allowing the reconstructive plastic surgeon who performs the surgery to get a close match to the existing ear.

A series of surgeries are needed for reconstruction of the ear. The surgeon takes grafts of cartilage from the ribs to build up the body of the ear, and grafts of skin to cover the ear. In a series of surgeries, the grafts will be encouraged to grow and sculpted by the surgeon to take on a realistic appearance. Once the surgeries are complete, the patient should have a very realistic replacement for the missing ear.

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Anotia and microtia both are caused by problems with the development of the ear in the fetal state. Signals get mixed, growth fails to happen, and the ear remains absent instead of developing, or does not develop normally, leading to microtia. This can be related to environmental exposure, as for example in the cases of babies born to mothers who took thalidomide during pregnancy, and sometimes a genetic condition can lead to anotia. In other cases, there are no clear causes, and something simply went awry during the development of the baby.

When selecting a surgeon to reconstruct the missing or malformed ear, it is a good idea to seek out a surgeon who has experience with patients who have anotia or microtia. Patients may also find it helpful to seek treatment at a hospital which specializes in caring for children with congenital conditions. A medical team can evaluate the child for any other signs of problems, providing prompt intervention while also addressing the missing ear.

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turquoise
Post 2

@ddljohn-- I think it depends on the specific situation. There was a girl from my town on the news last month. She was born with anotia and lived without ears for five years. In her case, she couldn't hear anything through either ear without a hearing aid.

She was on the news because she had surgery and they built her two ears and now she can hear perfectly. She doesn't even use her hearing aid anymore.

My mom's friend knows the family personally and she said that the surgery was really expensive. I think she said $50,000 per ear! I think that's too expensive!

ddljohn
Post 1

So, can someone who is born with anotia hear?

I don't know anyone who was born without ears, but I do have a pet rabbit who was born without them. I've always wondered if she can actually hear anything. We took her to the vet when she was first born and he wanted to do some expensive tests to figure it out but we couldn't afford it.

She seems fine otherwise, but I really can't tell if she can hear anything or not.

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